Extractions: PatientPlus articles are written for doctors and so the language can be technical. However, some people find that they add depth to the articles found in the other sections of this website which are written for non-medical people. This is a syndrome where the patient has multiple cognitive deficits and memory loss (enough to impair occupational or social functioning); with either associated deterioration in language (aphasia), perception and comprehension (apraxia); impaired ability to recognise objects (agnosia); and/or a disturbance in executive functioning (inability to think abstractly and plan, initiate, sequence, monitor and stop complex behaviour). Deterioration must represent a progressive decline from a previous higher level of functioning, and consciousness should not be clouded (cf acute confusional state, delirium). Memory loss is typically for recent events and long-term memory can be remarkably intact. Acute confusional state is of recent onset and usually has a reversible cause. Dementia is more chronic and usually untreatable. The onset may be less acute than at first apparent as the patient manages to cover the deficiency by making notes or bluff but when compensatory mechanisms fail deterioration appears more rapid than it really is. Causes of adult onset dementia: (not an exhaustive list) and mixed pathologies are common (33.8%)
Portal Toolkit Invalid Site URL Cerebral blood flow in spinocerebellar degenerations a single photon emissiontomography study in 28 patients. J Neurol 1998;2456038. Context Link http://ppv.ovid.com/pt/re/obes/fulltext.00000132-199911000-00006.htm
OMIM Entry 164600 earlier editions, it may be that linkage will provide the necessary methodfor unravelling the snarled nosology of the spinocerebellar degenerations. http://www.hgmp.mrc.ac.uk/cgi-bin/wrapomim?164600
Ataxia Rare Disorders . Spinocerebellar Degenerations Neurological Disorders . Conditions and Diseases . Health . Home Ataxia RareDisorders . spinocerebellar degenerations . Neurologic Manifestations . http://www.thema-gute-gesundheit.de/Health|DE-6404-6640|Conditions,and,Diseases|
Centre For Molecular Biology And Neuroscience Neurogenetics of spinocerebellar degenerations. Key features of neurodegenerativedisorders associated with triplets repeats and polyglutamine expansions, http://www.cmbn.no/seminar-20031212.html
Extractions: Fax: +47 22851488 Friday 12 December - Saturday 13 December 2003 Please confirm your attendance to by email to chantal.tallaksen@ulleval.no, or by fax to +47 22115949. Friday 12 December New tools and new challenges in neurogenetics Neurogenetics of spinocerebellar degenerations Key features of neurodegenerative disorders associated with triplets repeats and polyglutamine expansions, and implications for further research topics. Presentation of the Center for Molecular Biology and Neuroscience (CMBN) Novel DNA and RNA repair mechanisms DNA repair and genomic instability Glutamate transport and neurological disease
Vol20 Iss06 URL Http//www.flonnet.com/fl2006/stories Huntington s disease, Wilson s disease, spinocerebellar degenerations, Lewybody disease, idiopathic ganglia degenerations and so on. http://www.hinduonnet.com/thehindu/thscrip/print.pl?file=20030328001108000.htm&d
National University Corporation University Of Yamanashi Multiple system atrophies such as spinocerebellar degenerations and ShyDragersyndrome. Demyelinating diseases such as multiple sclerosis. http://www.yamanashi.ac.jp/english/medical/18sinkeinaika.html
Extractions: ▼Menu ■School of Medicine Department of Neurology Neurophysiology Analyses of autonomic nerve function in neurodegenerative disease using a microneurographic technique. Differentiation between physiologic and pathologic aging, mainly with respect to autonomic nerve function. Studies of the general effect on neurologic function from bathing in an artificially carbonated spring, including effects on pathologic states. Characterization of sleep disorders in neurologic disease, in relation to respiration and involuntary movements. Activities of afferent fibers from muscle spindles in neuromuscular diseases. Neuropathology Characterization of cerebrovascular pericytes in rats. Investigation of metabolism of prostaglandin D2 synthetic enzymes. Neuropathologic investigation of biopsy specimens of muscle and nerve. Neuropathologic investigation of Creutzfeldt-Jakob disease. Dementia and underlying degenerative diseases such as Alzheimer's disease and Pick's disease.
Cerebellum Diseases include hereditary spinocerebellar degenerations (such as Friedrich sataxia) and degenerative disease due to too much ethanol imbibition. http://instruct.uwo.ca/anatomy/530/cblm.htm
Extractions: The cerebellum: its parts and their connections. The cerebellum has three functional divisions, based on the principal sources of afferent fibres. The vestibulocerebellum (salmon pink, surrounded by a thin yellow line on the diagram) consists of the nodule and the two flocculi. Afferents are from the vestibular ganglion and nuclei. The spinocerebellum (light beige on diagram, and demarcated by a thick yellow line) consists of the vermis and adjacent cortex of the anterior lobe and of part of the posterior lobe. The dorsal and ventral spinocerebellar tracts terminate in these regions.
Extractions: Scientific Institute Eugenio Medea for Research, Hospitalization and Health Care Who we are Where Departments Pathologies ... Italian site Rehabilitation of Infantile Cerebral Palsy; Rehabilitation of neuromuscular diseases; Rehabilitation of acquired brain lesions; Study and rehabilitation of spinal and musculoskeletal disorders; Orthopaedic rehabilitation post-surgery; Rehabilitation of congenital and acquired bone marrow lesions; Rehabilitation of neurological bladder dysfunction Cognitive disorders and learning disabilities; Clinical psychology; Neurolinguistics and Psycholinguistics; Clinical and biological psychiatry Clinical and experimental neurophysiology; static and functional imaging. Chromosomal diseases; Biomolecular diagnostics; Genic Therapy; Biological Material Bank; Murine Transgenic models and Know-out Error analysis; Virtual reality; Application of Neuroimaging techniques; HW and SW development and aids; Development, experimentation and assessment of electro-medical devices; Tele-medicine; Support technologies for disabilities
HEALTHMEDNET ILLNESS DISEASE URL DIRECTORY Spinocerebellar degeneration see Friedreich s ataxia.http//www.nlm.nih.gov/medlineplus/encyclopedia.html. spinocerebellar degenerations http://www.healthmednet.com/SPIN-STE.htm
Myoclonus types of slowly progressive neurologic condions that may or may not run infamilies (eg. spinocerebellar degenerations, basal ganglia degenerations, http://www.cmdg.org/Movement_/myoclonus/myoclonus.htm
Extractions: The Canadian Movement Disorder Group MYOCLONUS Definition: A sudden "Shock" like muscular movement Myoclonus can be Classified By: 1) The Electrophysiologic Phenomenon (certain electrical characteristics) Negative Myoclonus (asterixis) a sudden relaxation of a group of muscles. 2) Classification by the Anatomical Origin Electical Discharge From the surface of the brain ( Cortical Myoclonus ).............Epileptic From deeper within the brain ( Subcortical Myoclonus From an electrical impulse within the spinal cord ( Spinal or Segmental Myoclonus From an electrical impulse within a peripheral nerve ( Peripheral Myoclonus eg. hemifacial spasm) 3) Classification byBody Parts Involved Focal If only one body part is affected myoclonus is called "focal" . (eg. myoclonic jerks of 1/2 the face ( "hemifacial spasm" ), or when the eyes are affected "Opsoclonus" Segmental If only one segment of the body is affected myoclonus is called "segmental"
Postgraduate Medicine: Primary Care Guide To Myoclonus And Chorea B. spinocerebellar degenerations C. Basal ganglia degenerations D. Dementias E.Infection or postinfectious syndromes F. Metabolic 1. Electrolyte disorders http://www.postgradmed.com/issues/2000/10_00/caviness.htm
Extractions: John N. Caviness, MD VOL 108 / NO 5 / OCTOBER 2000 / POSTGRADUATE MEDICINE CME learning objectives The author discloses no financial interests in this article. This is the third of four articles on hyperkinetic movement disorders This page is best viewed with a browser that supports tables. Preview : Myoclonic and choreic disorders encompass a wide range of manifestations, from simple jerking during sleep in neurologically normal persons to wild, potentially injurious flailing in patients with ballismus. Recognition of the type and cause of the disorder is the first step toward helping patients achieve better functioning when possible. Dr Caviness reviews classification of myoclonus and chorea and discusses appropriate evaluation and the available treatment options.
Extractions: New Delhi Dementia is a clinical syndrome characterized by acquired losses of cognitive and emotional abilities severe enough to interfere with daily functioning. Dementing illness is an important cause of disability in the elderly. With improving medical facilities and an increasing life expectancy, the number of patients with demential is expected to rise. The care of these patients will have a growing impact and will pose an increasing burden on the family, the health care systems and the society. Epidemiology The prevalence rates according to western studies range from 5-10 percent for all persons over the age of 65 years. These rates appear to double roughly every 5 years to reach 25-50 percent for persons over 85 years of age . The exact prevalence of these disorders in India is difficult to guess, as no recent population based prevalence study has been published. However, in a population-based survey reported in 1981, of 18,721 individuals, 861 were above the age of 60 years. Of these 181 randomly selected individuals, 6 percent were found to be demented . Most of the other studies conducted in India are inadequate as the validity of the criteria used to define and assess dementia needs to be questioned. Another confounding factor is the diversity of educational status and literacy in our population. There is also a general belief that the amount of vascular dementias (VaD) would outnumber the Alzheimer's dementias (AD) in our population.
Received From JNET-Daemon By UNCVX1.BITNET; Mon, 30 Mar 92 0818 in general, encompass a variety of degenerative disorders, interchangeablyreferred to as spinocerebellar degenerations, that are difficult to classify http://www.ibiblio.org/pub/docs/nih-nsf/nihguide2.920306
Humana Press Familial AdultOnset spinocerebellar degenerations, James H. Bower, md.Corticobasal Degeneration, Bradley F. Boeve, md. http://www.humanapress.com/ProductDetail.pasp?txtCatalog=HumanaBooks&txtCategory
Extractions: To know the diagnostic criteria for the diagnosis of dementia To list five causes of dementia To understand the importance of age-based norms when evaluating cognition in the elderly To recognize that there are reversible causes of dementia To name three basic tests used in the evaluation of possible dementia DEMENTIA DEFINITION A progressive loss of intellectual abilities of sufficient severity to interfere with social and/or occupational functioning. “Dementia” is a descriptive term, not a specific disease or condition. There are dozens of pathophysiologic causes of dementia. Because dementia is seen in the context of so many conditions, dementia is one of the most common findings encountered by neurologists who see adult patients. A. MAGNITUDE OF THE PROBLEM The population over 65 years of age is increasing rapidlyfrom 23 million in 1978 (11% of the population) to 51 million by 2030 (about 19% of the population). If life expectancy continues to rise, and the mean age of onset of dementia does not, some authors have projected that about 45% of the population would develop dementia at some point during their lives (with life expectancy extending into the late 90’s).