Entrez PubMed prune belly syndrome is a relatively uncommon disorder that is characterized byintrauterine urinary http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=PubMed&list_uids=8
Prune Belly Syndrome - General Practice Notebook prune belly syndrome is a rare and sporadic disease, occuring almost exclusivelyin boys only 3% of cases are female. The name refers to the appearence of http://www.gpnotebook.co.uk/cache/147849229.htm
UpToDate Prune-belly Syndrome INTRODUCTION The prunebelly (Eagle-Barrett) syndrome (PBS) is a The incidenceof the prune-belly syndrome is estimated at approximately 1 in 40000 to http://patients.uptodate.com/topic.asp?file=neonatol/24647&title=Constipation
Log In Problems A 17year-old Hispanic adolescent boy presented to the emergency department witha 6-hour history of right flank pain and hematuria. http://www.medscape.com/viewarticle/475287
Extractions: A 54-year-old man was diagnosed as having prune-belly syndrome, a deficiency of abdominal musculature, cryptorchidism, abnormalities of the urinary tract, and chronic renal failure. The patient was asymptomatic until the diagnosis was made at the age of 54 years; he is one of the oldest living patients to be reported in detail. Recognition of the syndrome in adults with chronic renal failure is important.
Extractions: This Article Submit a response Alert me when this article is cited Alert me when eLetters are posted Alert me if a correction is posted Services Email this article to a friend Similar articles in this journal Similar articles in PubMed Alert me to new issues of the journal ... Download to citation manager PubMed PubMed Citation Articles by Alford, B. A. Articles by L'Heureux, P. R. BA Alford, WM Peoples, JS Resnick and PR L'Heureux Eight patients are presented who demonstrate many of the pulmonary complications seen in the prune-belly syndrome. The patients are divided into two major groups: Group I includes pulmonary hypoplasia; Group II includes lobar atelectasis and pneumonia. The etiology, pathogenesis, and radiographic features of these complications are discussed. Pulmonary complications become more important as renal dialysis and transplantation spare more of these patients from an early uremic death. Prompt recognition
Extractions: This Article Submit a response Alert me when this article is cited Alert me when eLetters are posted Alert me if a correction is posted Services Email this article to a friend Similar articles in this journal Similar articles in PubMed Alert me to new issues of the journal ... Download to citation manager PubMed PubMed Citation Articles by Kirchner, S. G. Articles by Donnell, R. M. SG Kirchner, FK Kirchner Jr, H Jolles, RM Heller, RK Rhamy and RM Donnell
Extractions: This Article P Rs: Submit a response Alert me when this article is cited Alert me when P ... Alert me if a correction is posted Services E-mail this article to a friend Similar articles in this journal Similar articles in PubMed Alert me to new issues of the journal ... Cited by other online articles PubMed PubMed Citation Articles by Moerman, P. Articles by Lauweryns, J. M. P Moerman, JP Fryns, P Goddeeris and JM Lauweryns Abdominal muscle deficiency, urinary tract abnormalities, and cryptorchidism are the three major features of the prune-belly syndrome, also referred to as triad syndrome or Eagle-Barrett syndrome. The etiology is unclear and the pathogenesis a subject of continuing debate. Clinical and pathologic experience with seven cases of prune- belly syndrome is reviewed. Findings indicate that the urogenital anomalies can be attributed to a functional urethral obstruction which in turn is the result of prostatic hypoplasia. The histology of the abdominal wall is that of
Extractions: [Site éditeur Orphanet base de données sur les maladies rares et les médicaments orphelins. Direction Générale de la Santé / INSERM ; signes de la maladie, sites internet, dysmorphologie, conseil génétique, néphrologie pédiatrique ; pays : France ; langue : français ; format : html ; accès : gratuit ; non parrainé ; daté de : 2003 ; visité le : 11/09/2003].
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Extractions: Vol Page [Advanced] This Article Submit a response Alert me when this article is cited Alert me when eLetters are posted Alert me if a correction is posted Services Email this link to a friend Similar articles in ADC Online Similar articles in PubMed Alert me to new issues of the journal ... Download to citation manager PubMed PubMed Citation Articles by Crompton, C. Articles by Geary, D. CH Crompton, IB MacLusky and DF Geary Department of Pediatrics, Hospital for Sick Children, Toronto, Canada. Respiratory function was evaluated in 11 patients with prune-belly syndrome. Nine had evidence of gas trapping and six of restrictive lung disease. These abnormalities of lung function appear to be secondary to the musculoskeletal disorder associated with prune-belly syndrome rather than parenchymal lung disease.
Extractions: Vol. 131 No. 6, June 1977 Featured Link E-mail Alerts ARTICLE Article Options Send to a Friend Readers Reply Submit a reply Similar articles in this journal Literature Track Add to File Drawer Download to Citation Manager Articles in PubMed by Pramanik AK Sutherland JM Contact me when this article is cited A. K. Pramanik, G. Altshuler, I. J. Light and J. M. Sutherland Three fatal cases of prune-belly syndrome were associated with nonrenal features of Potter syndrome. The abdominal muscle hypoplasia is thought to be a result of large kidneys compression the developing abdominal musculature during a critical phase of fetal development. Thus, Potter syndrome and prune-belly syndrome may coexist when nonfunctioning large kidneys result in oligohydramnios. A teratogenic role of cytomegalovirus
