Birth Disorder Information Directory - V (Von mayer) rokitansky kuster (hauser) syndrome (MRK Anomaly; Uterus BipartitusSolidus Rudimentarius Cum Vagina Solida; Vaginal Atresia; Vagina, http://www.bdid.com/defectv.htm
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Vaginal Atresia RKH syndrome VON mayer rokitansky - kuster ANOMALY MRK ANOMALY See vagina,absence of ( rokitansky - kuster - hauser syndrome; 277000 ) mayer http://ibis-birthdefects.org/start/vaginal.htm
Extractions: Shokeir (1978) described 28 unrelated females, aged 15 to 28, with aplasia of the mullerian duct derivatives. Their complaints were amenorrhea and difficulty or pain on attempting sexual intercourse; absence of the vagina and failure to palpate the uterus rectally were features in all ... The pedigree pattern was consistent with female - limited autosomal dominant inheritance. The disorder was transmitted through normal males. See vagina, absence of ( Rokitansky - Kuster - Hauser syndrome; 277000 ) ...
Extractions: Välkommen till min sida som handlar om ett intersexsyndrom som förtjänar lite mer uppmärksamhet Presentation Beskrivning Historia Behandling ... Länkar Mayer-Rokitansky-Küster-Hauser Syndrome Kallas även för Müllersk agenesis, vaginal- och livmoderagenesis /-aplasi H är har jag samlat lite information om ett intersexsyndrom som inte är särskilt känt. MRKH är relativt ovanligt och återfinns hos ca 1 av 5 000 kvinnor. Syndromet innebär att man saknar livmoder och vagina. M R K H Syndrome Maila Till Mig
Extractions: Each question will be responded to after the subject has been carefully investigated. However, Frontiers in Bioscience merely provides the information as a general guide to help patients and with the understanding that the contributors can not accept any type of liability for the use of the information. The information can not substitute expert medical advice and should be regarded as the starting point for finding the proper medial treatment. Questions are subject to editorial corrections. Question: I am seeking information regarding the treatment and postoperative management of Rokitansky syndrome. My 17 year-old daughter was recently diagnosed with this disorder, and we need help deciding what the treatment options, and the postoperative outcome may be. References from Medline MEDLINE reports MEDLINE abstracts MEDLARS reports ASN.1 reports MEDLINE neighbors protein links nucleotide links structure links genome links Back into Entrez for All Selected articles below. van Bever, 1992
The Journal Of Urology - UserLogin Vaginal atresia in patients with mayerrokitansky-kuster-hauser syndrome is causedby aplasia of the müllerian ducts. The anomaly has various presentations. http://www.jurology.com/pt/re/juro/fulltext.00005392-200309000-00040.htm
Extractions: Abstract PDF (33 K) References (9) View full size inline images The Journal of Urology Volume 162(3-II) September 1999 pp 1138-1139 DEL ROSSI, CARMINE; ATTANASIO, ANNA; DOMENICHELLI, VINCENZO; DE CASTRO, ROBERTO From Saint Mary's Sick Assistance Center, Khulna, Bangladesh, and Division of Pediatric Surgery, Azienda Ospedaliera, Parma, European Institute of Oncology, Milan and Department of Pediatric Surgery, Bologna University Medical School, Bologna, Italy Article Outline Citing Articles Figures/Tables Purpose: We report our experience with treating the Mayer-Rokitansky-Kuster-Hauser syndrome in a developing country. The operations were performed by a pediatric surgical team at a missionary hospital in Khulna, Bangladesh. Materials and Methods : From 1995 to 1998, 10 young women with the Mayer-Rokitansky-Kuster-Hauser syndrome underwent complete vaginal replacement. In 4 patients the abnormality was discovered after marriage at the initial sexual approach and, thus, the husband abandoned 3. In 4 of the 10 cases the diagnosis was suspected because of absent menstruation. A physician made the diagnosis in only 2 cases. Preoperatively abdominal ultrasound in 3 patients showed a hypoplastic uterus in all and a right solitary pelvic kidney in 1. In all 10 women a neovagina was created using a 14 cm. segment of sigmoid colon. Two weeks postoperatively patients were taught to dilate and irrigate the neovagina.
Journal Of Pelvic Medicine & Surgery - UserLogin mayerrokitansky-kuster-hauser syndrome Presenting as an Inguinal Mass and Herniain the Female Patient. Bidus, Michael A. MD, LCDR, MC, USNR*; Martin, http://www.jpelvicsurgery.com/pt/re/spv/fulltext.00146866-200407000-00002.htm
Extractions: Objectives: Complete mullerian agenesis is the second most common condition usually diagnosed during a work-up for primary amenorrhea. A detailed gynecologic history and pelvic examination are the foundations for establishing the diagnosis. Methods: An 18-year-old nulligravida presented to the General Surgery Service complaining of right-sided lower abdominal pain. Upon dissection of the right inguinal canal, it was noted that the hernia sac contained the right ovary and fallopian tube. An intraoperative consult to the Gynecology Service was obtained. The hernia was reduced and the ovary returned to the pelvis. Pelvic examination under anesthesia revealed a severely shortened vagina. A diagnostic laparoscopy was performed revealing complete mullerian agenesis. Postoperative evaluation included a normal karyotype and normal intravenous pyelogram (IVP). Results: The differential diagnosis of inguinal masses in women should include mullerian tract abnormalities.
Indigopedia:MRKH - IndigoWiki MRKH An acronym for mayerrokitansky-kuster-hauser syndrome, a relativelyrare (15000 female births) condition marked by primary Amenorrhoea, http://wolfandturtle.net/Indigo/index.php/Indigopedia:MRKH
Extractions: edit Retrieved from " http://wolfandturtle.net/Indigo/index.php/Indigopedia:MRKH Categories Indigopedia Views Personal tools Navigation Search Toolbox What links here Related changes Upload file Special pages ... Printable version This page has been accessed 149 times. This page was last modified 20:01, 1 February 2005 by Myria About IndigoWiki
Extractions: For Researchers For Librarians Authors: Marwah V.; Bhandari S.K. Source: The Journal of the American Association of Gynecologic Laparoscopists , Volume 8, Number 3, 1 August 2001, pp. 416-424(9) Publisher: American Association of Gynaecological Laparoscopists View Table of Contents full text options Abstract: Document Type: Original article The full text article is available for purchase $30.00 plus tax The exact price (including tax) will be displayed in your shopping cart before you check out. You will be able to remove this item from your shopping cart at any time before you have completed check-out. View Table of Contents Back to top Terms and Conditions Page Help Quick Search
Hum. Reprod. -- Sign In Page mayervon rokitanskyKüsterhauser syndrome (MRKHS) is characterized by thecongenital absence of the vagina and a variety of Müllerian duct anomalies, http://humrep.oxfordjournals.org/cgi/content/full/19/5/1201
Extractions: This item requires a subscription* to Human Reproduction Online. * Please note that articles prior to 1996 are not normally available via a current subscription. In order to view content before this time, access to the Oxford Journals digital archive is required. Alternatively, you may purchase short-term access on a Pay per Article basis. Please see below for more details. This Article Abstract Full Text (PDF ) Alert me when this article is cited ... Alert me if a correction is posted Services Email this article to a friend Similar articles in this journal Similar articles in ISI Web of Science Similar articles in PubMed ... Request Permissions PubMed PubMed Citation Articles by Ulrich, U. Articles by Rhiem, K. To view this item, select one of the options below: Sign In User Name Sign in without cookies.
Extractions: Service de Chirurgie Gynecologique, Clinique Universitaire Baudelocque, C.H.U. Cochin Port-Royal, Paris, France. Mayer-Rokitansky-Kuster-Hauser (MRKH) syndrome is a partial or complete absence (agenesis) of the uterus with an absent or hypoplastic vagina. Until now, the recommended treatment, when resection of a rudimentary horn was indicated, was laparotomy. We report a case of MRKH syndrome in which
Forum Médical - Syndrôme De Mayer Rokitansky Kuster Hauser Translate this page Le syndrome de mayer rokitansky kuster hauser est le motif de 1/20 000 consultationsdans les services de gynécologie hospitaliers. http://forums.remede.org/externat_et_ecn/sujet_4609.html
AIS (Androgen Insensitivity Syndrome) Support Group 5alpha-reductase deficiency, Leydig cell Hypoplasia,mayer-rokitansky-kuster-hauser (MRKH) syndrome, Mullerian dysgenesis, Mullerianduct aplasia, http://www.medhelp.org/www/ais/
Extractions: Androgen Insensitivity Syndrome AIS is a condition that affects the development of reproductive and genital organs. Both men and women usually have at least one X chromosome, which contains a gene that gives their bodies the capacity to recognise and react to masculinizing hormones (androgens). Men usually have a Y chromosome as well, which codes for the production of androgens and the inhibition of female internal organ development. Women with AIS have a functioning Y chromosome (and therefore no female internal organs), but an abnormality in the X chromosome that renders the body partially or completely incapable of recognising the androgens produced, therefore allowing the default external genital development along female lines. Other related conditions, based on different chromosomes, also disrupt the normal pathway of androgen action, resulting again in a female phenotype. The Support Group We are a support group providing information and support to young people and adults with complete and partial Androgen Insensitivity Syndrome, and to parents of AIS youngsters. We also support those affected by Swyer's syndrome (XY gonadal dysgenesis), 5-alpha-reductase deficiency, Leydig cell Hypoplasia, Mayer-Rokitansky-Kuster-Hauser (MRKH) syndrome, Mullerian dysgenesis, Mullerian duct aplasia, vaginal atresia, and other related conditions. Please note that AIS is also known as Testicular Feminisation (or Feminization).
