Mayo Clinic Proceedings Katz SK, Mudd LJ, Roenigk HH Jr. malignant atrophic papulosis (Degos disease)involving three generations of a family. J Am Acad Dermatol. http://www.mayoclinicproceedings.com/inside.asp?AID=17&UID=
Degos' Disease Information Diseases Database malignant atrophic papulosis. may cause or feature + (Follow link for list.)belong(s) to the category of + (Follow link for list.) No UMLS definitions.. http://www.diseasesdatabase.com/ddb29425.htm
American Family Physician: Dermatomyositis malignant atrophic papulosis (Degos disease). Zebralike striping. Vulvar/scrotalinvolvement. Heliotrope, a macular rash with periorbital edema, http://www.findarticles.com/p/articles/mi_m3225/is_9_64/ai_80099707
Extractions: Save a personal copy of this article and quickly find it again with Furl.net. It's free! Save it. Dermatomyositis is an idiopathic inflammatory myopathy with characteristic skin manifestations. Although the disorder is rare, with a prevalence of one to 10 cases per million in adults and one to 3.2 cases per million in children, early recognition and treatment are important ways to decrease the morbidity of systemic complications. An association with other connective tissue disorders (overlap syndrome) and malignancy make this diagnosis particularly important to primary care physicians. Patient management includes careful evaluation for underlying malignancy and liberal use of physical therapy, antihistamines, sunscreen and oral corticosteroids. Poor prognostic indicators include poorly responsive disease, delay in diagnosis and the presence of malignancy. The therapeutic goal is to maintain function and prevent or minimize sequelae. (Am Fam Physician 2001;64:1565-72.)
Degos Disease Degos disease, also known as malignant atrophic papulosis is a rare disorder.It affects the lining of the small blood vessels resulting in blockage. http://www.betterhealth.vic.gov.au/bhcv2/bhcarticles.nsf/pages/Degos_disease?Ope
Extractions: printer friendly home how we can help medical information ... how you can help Please use the index below to access the condition you require information on. It may take longer to find what you are looking for this way compared with our "search this site" facility in the navigator on the left but we try to point you in the most appropriate direction using this index and therefore the results should be better. For speed, this index has been split into separate alphabetical files: numbers 0-9 A B C ... Z Contact a Family also has information on many other specific conditions and rare disorders. If you cannot find the information you require in The Contact a Family Directory Online , you may wish to use our Contact a Family Helpline service. MAD see Fatty Acid Oxidation Disorders
Extractions: helpful? yes no Degos disease: Malignant Atrophic Papulosis: Kohlmeier-Degos disease Degos disease is a rare inherited condition first described by Kohlmeier in 1941 and Degos in 1942. There are thought to have been about 150 cases of the condition reported in medical literature. The most severe form is Systemic Degos disease affecting children and adolescents with most cases occurring in young adults. Benign Degos disease also affects adults. Systemic Degos disease affects a number of body systems: Skin - pink or red papules (solid raised lesions) primarily on the trunk and limbs healing to leave white scars; Gastrointestinal - abdominal pain, nausea, vomiting, diarrhoea or constipation and, in the later stages, intestinal perforation and haemorrhage may occur; Neurological - manifestations involve the peripheral and central nervous systems leading to headaches, dizziness, seizures, hemiplegia (total or partial paralysis of one side of the body), aphasia (loss or impairment of the power to use or comprehend words), paraplegia (paralysis of the lower half of the body), and gaze palsy (partial or complete inability to move the eyes to all directions of gaze); Ocular - ptosis (drooping of the upper eyelid), optic neuritis (inflammation of optic nerves), diplopia (double vision) and visual field defects may occur.
UWCM Department Of Dermatology malignant atrophic papulosis (Degos disease) clinicopathological correlations.JEADV 2001; 15 4345. Chowdhury MMU, Chakrabarti A, Prais L, http://www.dermatology.org.uk/portal/asp/pubs0102.html
Extractions: Research Papers Anstey AV. Photomedicine: Lessons from the Smith-Lemli-Opitz syndrome. J Photochemistry Photobiology 2001; 62: 123-7 Azurdia RM, Anstey AV, Rhodes LE. High cholesterol diet improves the photosensitivity in Smith-Lemli-Opitz syndrome. Br J Dermatol 2001; 144: 143-5 Chave T A, Varma S, Patel G K, Knight A G .Malignant atrophic papulosis (Degos' disease): clinicopathological correlations. JEADV 2001; 15: 43-45. Chowdhury M M U, Chakrabarti A, Prais L, Foulds I S. Occupational allergic contact dermatitis caused by 5,7-dichloro-4(4-fluorophenoxy) quinolone (quinoxyfen). Contact Dermatitis 2001; 45: 119-20. Chowdhury M M U, Motley R J. Treatment of acrodermatitis continua of Hallopeau with oral propylthiouracil and methotrexate. Clin Exp Dermatol 2001; 26: 657-60. Chowdhury M M U, Statham B N. Allergic contact dermatitis from dibutyl phthalate and benzalkonium chloride in Timodine®. Contact Dermatitis 2002; 46: 57. Chowdhury M M U, Inaloz H S, Motley R J, Knight A G. Erythema elevatum diutinum and IgA paraproteinaemia: 'a preclinical iceberg'. Int J Dermatol 2002; 41: 368-70.
Extractions: Research Papers ANSTEY AV. Drug reactions and the skin. Medicine 2000; 28: 12: 63-64. CHAVE TA, CHOWDHURY MMU, HOLT PJA. Recalcitrant necrobiotic xanthogranuloma responsive to pulsed oral dexamethasone and maintenance prednisolone. Br J Dermatol 2001; 144: 158-61. CHAVE TA, FINLAY AY, KNIGHT AG - On behalf of the All Wales Dermatology Audit Committee. Thalidomide usage in Wales: the need to follow guidelines. Br J Dermatol 2001; 144: 310-315. CHAVE T, VARMA S, LOGAN R, HOLT PJA. A papillary lesion on the foreskin. Arch Dermatol 2001; 137: 815-20 (off-centre). CHAVE TA, VARMA S, PATEL GK, KNIGHT AG. Malignant atrophic papulosis (Degos' disease): clinicopathological correlations. J Eur Acad Dermatol Venereol 2001; 15: 43-45. CHOWDHURY MMU. The management of psoriasis in primary care. Prescriber 2000; 11(18): 99-107. CHOWDHURY MMU, ANSTEY AV. Dermatological Pharmacology. Medicine 2000; 28(11): 12-16. CHOWDHURY MMU, ANSTEY A, MATTHEWS CAN. The dermatosis of chronic granulomatous disease. Clin Exp Dermatol: 2000; 25:190-4.
Portal Toolkit Invalid Site URL CNS involvement in malignant atrophic papulosis (KohlmeierDegos disease)vasculopathy and coagulopathy. J Neurol Neurosurg Psychiatry 1981 44 156-160. http://ppv.ovid.com/pt/re/obes/fulltext.00000132-199611000-00010.htm
All Topics - Quest Diagnostics Patient Health Library Degos Disease (malignant atrophic papulosis) Support Group. Degos PatientsSupport Network Degos Disease (malignant atrophic papulosis) Support Group http://www.questdiagnostics.com/kbase/list/all/d.htm
Extractions: DA Da Costa's Syndrome Dacryosialoadenopathia Dacryosialoadenopathy DAD-to-DAD - Parenting / Grandparenting [Support Group] Dalpro, Fetal Effects From Dana Farber Cancer Institute Family Studies Cancer Risk Line - Cancer Helpline [Support Group] Danazol [Medication] Danazol for endometriosis [Medication] Danazol for severe PMS (premenstrual dysphoric disorder) [Medication] Danbolt-Cross Syndrome Dancing Eye Syndrome [Support Group] Dancing Eye Syndrome - Dancing Eye Syndrome [Support Group] Dandruff Dandruff Dandy Fever Dandy Walker Malformation ... Dandy Walker Syndrome [Support Group] Dandy-Walker Cyst Dandy-Walker Deformity Dandy-Walker Syndrome Dandy-Walker Syndrome Network - Dandy Walker Syndrome [Support Group] Danish Cardiac Type Amyloidosis (Type III) Darier Disease Darier-White Disease Top Davidson's Disease Davies' Disease Dawson's Disease Dawson's Encephalitis ... Daycare
Postgraduate Medicine: Return Of The Painful Leg Ulcers subungual splinter hemorrhages, blue toe syndrome, malignant atrophic papulosis,and porcelainwhite scars (ie, atrophie blanche) (1). http://www.postgradmed.com/issues/2002/04_02/puzzles_answer.htm
Extractions: A ntiphospholipid-antibody syndrome (APS) is a multisystem disorder characterized by arterial or venous thrombosis, thrombocytopenia, recurrent fetal loss, and persistently elevated levels of antiphospholipid antibodies (1). Antiphospholipid antibodies are a heterogeneous group of circulating autoantibodies that includes anticardiolipin and anti-beta -glycoprotein I antibodies, which react with phospholipid-protein complexes, and lupus anticoagulants, which interfere with phospholipid-dependent coagulation reactions (2). APS may occur as either a primary disorder or a secondary disorder associated with (1) an underlying systemic disorder, including immunologic disease (most commonly systemic lupus erythematosus [SLE]), cancer, hematologic disease, infection, and neurologic disease, or (2) use of specific drugs (eg, procainamide hydrochloride, chlorpromazine hydrochloride and other phenothiazine derivatives, phenytoin, quinidine, streptomycin sulfate, clozapine) (1,2). Studies of patients with lupus anticoagulants have found that 50% of patients had SLE, while the remainder had various aforementioned disorders (1). Anticardiolipin antibodies are elevated in the presence of a diverse group of infectious agents, including HIV, whereas lupus anticoagulant in patients with HIV infection occurs more commonly with opportunistic infections and tends to disappear when the infection is treated (1).
: The AMEDEO Literature Guide Lesions resembling malignant atrophic papulosis in a patient with progressivesystemic sclerosis. Cutis 2005;751014. PubMed Related articles Abstract http://www.amedeo.com/medicine/skd/skd3.htm
Cutis Lesions Resembling malignant atrophic papulosis in a Patient With ProgressiveSystemic Sclerosis Liu CM, Harris RM, Hansen CD Abstract PDF http://www.cutis.com/asp/archive/pasttoc.asp?issuemonth=2&issueyear=2005
The American Journal Of The Medical Sciences - UserLogin presentation of HIV infection, 3 and malignant atrophic papulosis, which causesinfarctive thrombosis of the skin and viscera, has been reported. http://www.amjmedsci.com/pt/re/ajms/fulltext.00000441-200012000-00005.htm
MUMS List Of Disorders - M malignant atrophic papulosis(Degos disease) www.degosdisease.com; MalignantHyperthermia (12) *; Malrotation of the Intestines (31) http://www.netnet.net/mums/mum_m.htm
Extractions: indicates there is a support group which covers that diagnosis. MELAS Mitochondrial Encephalopathy Lactic Acidosis Syndrome (7) * Macrocephaly (large head) (29) http://www.macrocephaly-cmtc.com/ Macrodactyly (Large toes or fingers) (2) Macroglossia (6) Macrosomia (abnormally large body) (2) Macular Degeneration (4) * Macular Degeneration (Infantile) * Male Pseudohermaphroditism (2) * Malignant Atrophic Papulosis(Degos disease) www.degosdisease.com Malignant Hyperthermia (12) * Malrotation of the Intestines (31) Mandibuloacral Dysplasia(Craniomandibular Dermatodysostis) (3) Manic Depression, Bipolar (64) * Manic Depressive Schizophrenia (19) * Mannosidosis (Glycogen Storage) (4)** Maple Syrup Urine Disease (7) * Marcus Gunn Phenomenon (Jaw Winking) (3) Marden-Walker Syndrome (7) Marfan Syndrome (12) * Marinesco-Sjogren Syndrome (1) www.marinesco-sjogren.org Marshall-Smith Syndrome (1) Mast Cell Disease (Urticaria Pigmentosa) (9) Mastocytosis (Urticaria Pigmentosa) (9) www.mastokids.org
MUMS List Of Disorders - D - E Bjornstad Type (1); Degos disease (malignant atrophic papulosis)www.degosdisease.com; DejerineSottas Disease (Sensory Motor Neuropathy III) (6)* http://www.netnet.net/mums/mum_d-e.htm
Extractions: indicates there is a support group which covers that diagnosis. D-2Hydroxyglutaric Aciduria (2) DOORS Syndrome (4) DPT (damage from vaccine) (306) * Dandy-Walker Syndrome (68) * Darier Disease (1) * Darrow-Gamble Syndrome(Congenital Chloride Diarrhea) (1) * De Barsy Syndrome (lacking elasticity in skin) (2) DeMorisier Dysplasia Olfactorgenitalis (Kallmann Syndrome) (5) * Deaf/Blindness (71) * www.deafblindinfo.org Deaf/Blindness from Polio Vaccine (1) * Deafness (195) * Deafness-Pili-Torti, Bjornstad Type (1) Degos disease (Malignant Atrophic Papulosis) www.degosdisease.com Dejerine-Sottas Disease (Sensory Motor Neuropathy III) (6)* Delleman-Oorthuys Syndrome (1) Dentatorubral-Pallidoluysian Atrophy (DRPLA) (1) Dermatitis, Atopic (1) Dermatomyositis (15) * Desanctis-Cacchione Syndrome (Xeroderm Pigmentosum) (7) Developmentally Delayed (2735) * http://groups.yahoo.com/group/childdevdelays/ Dextrocardia (heart on right side) (34) * Dextrocardia with Situs Inversus (organs backward) (13) Dextrocardia-Bronchiectasis-Sinusitis Syndrome (Kartagener) (11) DiGeorge Syndrome (49) ** DiGeorge Syndrome and Klinefelter Syndrome (1) Diabetes, Gestational (5) *
Vasculitis Degos Disease is a rare disease, also known as malignant atrophic papulosis,initially presenting as a skin condition characterised by red papules with http://omni.ac.uk/browse/mesh/D014657.html
Extractions: low graphics broader: Vascular Diseases other: Aneurysm Angioneurotic Edema Arteriovenous Malformations Cerebrovascular Disorders ... Varicose Veins narrower: Behcet Syndrome Mucocutaneous Lymph Node Syndrome Thromboangiitis Obliterans Vasculitis This interactive tutorial on vasculitis, a group of diseases that causes blood vessels to become inflamed, has been produced by the Patient Education Institute, and made available on the Web by the National Library of Medicine MEDLINEplus service. The tutorial provides background information on vasculitis and covers causes, clinical signs and symptoms, diagnosis, and treatment. Viewing this tutorial requires Flash plug-in. Vasculitis Teaching Materials Patient Education Degos disease This is the Web site of the Degos Patients Support Network. Degos Disease is a rare disease, also known as malignant atrophic papulosis, initially presenting as a skin condition characterised by red papules with white centres, and telangiectasia. Serious (possibly fatal) gastrointestinal and neurologic symptoms usually follow. This Web site brings together what little is know about the condition, providing information for patients and clinicians on symptoms, diagnosis treatment and prognosis. Vasculitis Thromboangiitis Obliterans
