Extractions: You are in All Conditions ADD/ADHD Allergies Alzheimer's Arthritis Asthma Back Pain Bipolar Disorder Breast Cancer Cancer Cholesterol Management Dental Depression Diabetes Epilepsy Eye Health Heart Disease Hepatitis HIV/AIDS Hypertension Men's Conditions Mental Health Migraines/Headaches Multiple Sclerosis Osteoporosis Parkinson's Sexual Conditions Stroke Weight Control Women's Conditions Degos disease is a rare systemic disorder that affects small and medium sized arteries, causing them to become blocked (occlusive arteriopathy). Degos disease usually progresses through two stages. During the first stage, characteristic skin lesions appear that may last for a period of time ranging from weeks to years. The second stage of Degos disease is most frequently characterized by lesions in the small intestine, but other organs may also be affected. Major symptoms may include abdominal pain, diarrhea, and/or weight loss. Intestinal lesions may break through the wall of the bowel (perforation), a potentially life-threatening complication. The exact cause of Degos disease is unknown.
Index Kohler s Disease (of the Tarsal Navicular) Kohler s Osteochondrosis of theTarsal Navicular kohlmeierdegos disease Kok Disease Korsakoff s Syndrome http://my.webmd.com/hw/index/index-topics-K.asp
CNS Involvement In Malignant Atrophic Papulosis (Kohlmeier-Degos CNS involvement in malignant atrophic papulosis (kohlmeierdegos disease) vasculopathy and coagulopathy DK Dastur, BS Singhal and HJ Shroff http://tmsyn.wc.ask.com/r?t=an&s=hb&uid=24312681243126812&sid=343126
Extractions: It is possible that the main title of the report Degos Disease is not the name you expected. Please check the synonyms listing to find the alternate name(s) and disorder subdivision(s) covered by this report. Degos disease is a rare systemic disorder that affects small and medium sized arteries, causing them to become blocked (occlusive arteriopathy). Degos disease usually progresses through two stages. During the first stage, characteristic skin lesions appear that may last for a period of time ranging from weeks to years. The second stage of Degos disease is most frequently characterized by lesions in the small intestine, but other organs may also be affected. Major symptoms may include abdominal pain, diarrhea, and/or weight loss. Intestinal lesions may break through the wall of the bowel (perforation), a potentially life-threatening complication. The exact cause of Degos disease is unknown. Digestive Disease National Coalition
Kypros-Net ESearch Degos Patients' Support Network Advice, support, news, and a forum for patients with Degos disease (Malignant Atrophic Papulosis), their families http://tmsyn.wc.ask.com/r?t=an&s=hb&uid=24312681243126812&sid=343126
Diagnosing Degos - DegosDisease.com Burrow JN, Blumbergs PC, Iyer PV kohlmeierdegos disease a multisystem Sotrel A, Lacson AG, Huff KR Childhood kohlmeier-degos disease with atypical http://www.degosdisease.com/information/forpros/diagnosing-degos/synonyms_relate
Extractions: Degos disease (malignant atrophic papulosis) is a rare progressive, small and medium size arterial occluding disease, leading to tissue infarction initially involving the skin and later the gastrointestinal, ocular and central nervous systems. The disease is characterized by papules that develop porcelain-white centres and telangiectatic borders. This is the clue to the underlying disease which can affect the gastrointestinal tract and central nervous system and may lead to death. The skin biopsy places the pathologist at the centre of the diagnostic evaluation. In 1941, in an article entitled "Multiple Hautrekrosen bei Thromboangiitis obliterans," Kohlmeier described a case of a disease that has now been termed malignant atrophic papulosis (MAP) or Degos disease (DD). Degos recognized it as a distinct clinical entity in 1942. Broadly speaking, DD is a vasculopathy or an endovasculitis. It is an occlusive arteriopathy involving small-calibre vessels. Specifically, it is a progressive, small- and medium-size arterial occluding disease, leading to tissue infarction and initially involving the skin. DD occurs both in a limited benign, cutaneous form and in a lethal multiorgan, systemic variant. In the skin, DD initially manifests with erythematous, pink or red papules. These papules heal to leave scars with pathognomonic, central, porcelain white atrophic centers. These papules usually have a peripheral telangiectatic rim.
Malignant Atrophic Papulosis (Kohlmeier-Degos Disease) In Malignant atrophic papulosis (kohlmeierdegos disease) in childhood FA Horner, GJ Myers, DA Stumpf, BJ Oseroff and BH Choi http://tmsyn.wc.ask.com/r?t=an&s=hb&uid=24312681243126812&sid=343126
Extractions: Vol Page [Advanced] This Article Submit a response Alert me when this article is cited Alert me when eLetters are posted Alert me if a correction is posted Services Email this link to a friend Similar articles in this journal Similar articles in PubMed Alert me to new issues of the journal ... Cited by other online articles PubMed PubMed Citation Articles by Dastur, D. K. Articles by Shroff, H. J. Journal of Neurology, Neurosurgery, and Psychiatry, 1981, Vol 44, 156-160 DK Dastur, BS Singhal and HJ Shroff
JNNP Online -- Table Of Contents (44 [2]) CNS involvement in malignant atrophic papulosis (kohlmeierdegos disease)vasculopathy and coagulopathy DK Dastur, BS Singhal, and HJ Shroff http://jnnp.bmjjournals.com/content/vol44/issue2/
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Entrez PubMed A 45 year old female patient presented with the cutaneous manifestations ofmalignant atrophic papul http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=PubMed&list_uids=1
Entrez PubMed kohlmeierdegos disease, or malignant atrophic papulosis, is a rare and clinicallydistinctive vascu http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=PubMed&list_uids=2
Extractions: helpful? yes no Degos disease: Malignant Atrophic Papulosis: Kohlmeier-Degos disease Degos disease is a rare inherited condition first described by Kohlmeier in 1941 and Degos in 1942. There are thought to have been about 150 cases of the condition reported in medical literature. The most severe form is Systemic Degos disease affecting children and adolescents with most cases occurring in young adults. Benign Degos disease also affects adults. Systemic Degos disease affects a number of body systems: Skin - pink or red papules (solid raised lesions) primarily on the trunk and limbs healing to leave white scars; Gastrointestinal - abdominal pain, nausea, vomiting, diarrhoea or constipation and, in the later stages, intestinal perforation and haemorrhage may occur; Neurological - manifestations involve the peripheral and central nervous systems leading to headaches, dizziness, seizures, hemiplegia (total or partial paralysis of one side of the body), aphasia (loss or impairment of the power to use or comprehend words), paraplegia (paralysis of the lower half of the body), and gaze palsy (partial or complete inability to move the eyes to all directions of gaze); Ocular - ptosis (drooping of the upper eyelid), optic neuritis (inflammation of optic nerves), diplopia (double vision) and visual field defects may occur.
