1. Degos Disease Degos Syndrome; DegosKohlmeier Disease; kohlmeier-degos disease; Malignant AtrophicPapulosis. Disorder Subdivisions. None. General Discussion http://my.webmd.com/hw/heart_disease/nord991.asp

var guid_source = ""; var guid_source_id = ""; //unused var encodedurl = ""; WebMD Today Home WebMD News Center XML News via RSS Member Services WebMD University My WebMD Find a Physician Medical Info Check Symptoms Medical Library Health Tools Clinical Trials ... Women, Men, Lifestyle Who We Are About WebMD Site Map You are in All Conditions ADD/ADHD Allergies Alzheimer's Arthritis Asthma Back Pain Bipolar Disorder Breast Cancer Cancer Cholesterol Management Dental Depression Diabetes Epilepsy Eye Health Heart Disease Hepatitis HIV/AIDS Hypertension Men's Conditions Mental Health Migraines/Headaches Multiple Sclerosis Osteoporosis Parkinson's Sexual Conditions Stroke Weight Control Women's Conditions Health Topics Symptoms Medical Tests Medications ... For a Complete Report Degos Disease Important It is possible that the main title of the report Degos Disease is not the name you expected. Please check the synonyms listing to find the alternate name(s) and disorder subdivision(s) covered by this report. Synonyms Degos Syndrome Degos-Kohlmeier Disease Kohlmeier-Degos Disease Malignant Atrophic Papulosis Disorder Subdivisions None General Discussion Degos disease is a rare systemic disorder that affects small and medium sized arteries, causing them to become blocked (occlusive arteriopathy). Degos disease usually progresses through two stages. During the first stage, characteristic skin lesions appear that may last for a period of time ranging from weeks to years. The second stage of Degos disease is most frequently characterized by lesions in the small intestine, but other organs may also be affected. Major symptoms may include abdominal pain, diarrhea, and/or weight loss. Intestinal lesions may break through the wall of the bowel (perforation), a potentially life-threatening complication. The exact cause of Degos disease is unknown.

2. Degos Disease Degos Syndrome Degos-Kohlmeier Degos Disease Degos Syndrome DegosKohlmeier Disease kohlmeier-degos disease Malignant Atrophic Papulosis Degos Disease Degos http://tmsyn.wc.ask.com/r?t=an&s=hb&uid=24312681243126812&sid=343126

3. Index Kohler s Disease (of the Tarsal Navicular) Kohler s Osteochondrosis of theTarsal Navicular kohlmeierdegos disease Kok Disease Korsakoff s Syndrome http://my.webmd.com/hw/index/index-topics-K.asp

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4. CNS Involvement In Malignant Atrophic Papulosis (Kohlmeier-Degos CNS involvement in malignant atrophic papulosis (kohlmeierdegos disease) vasculopathy and coagulopathy DK Dastur, BS Singhal and HJ Shroff http://tmsyn.wc.ask.com/r?t=an&s=hb&uid=24312681243126812&sid=343126

5. Recurrent Pleural Effusions In Systemic Malignant Atrophic Your browser does not support frames. Click here to view the unframed reprint. http://tmsyn.wc.ask.com/r?t=an&s=hb&uid=24312681243126812&sid=343126

6. Recurrent Pleural Effusions In Systemic Malignant Atrophic Papulosis COPYRIGHT 2004 by the American College of Chest Physicians. http://tmsyn.wc.ask.com/r?t=an&s=hb&uid=24312681243126812&sid=343126

7. Degos Disease Synonyms. Degos Syndrome; DegosKohlmeier Disease; kohlmeier-degos disease;Malignant Atrophic Papulosis. Disorder Subdivisions. None. General Discussion http://www.bchealthguide.org/kbase/nord/nord991.htm

var hwPrint=1;var hwDocHWID="nord991";var hwDocTitle="Degos Disease";var hwRank="1";var hwSectionHWID="nord991-Header";var hwSource="en-caQ2_05";var hwDocType="Nord"; National Organization for Rare Disorders, Inc. Degos Disease Important It is possible that the main title of the report Degos Disease is not the name you expected. Please check the synonyms listing to find the alternate name(s) and disorder subdivision(s) covered by this report. Synonyms Degos Syndrome Degos-Kohlmeier Disease Kohlmeier-Degos Disease Malignant Atrophic Papulosis Disorder Subdivisions None General Discussion Degos disease is a rare systemic disorder that affects small and medium sized arteries, causing them to become blocked (occlusive arteriopathy). Degos disease usually progresses through two stages. During the first stage, characteristic skin lesions appear that may last for a period of time ranging from weeks to years. The second stage of Degos disease is most frequently characterized by lesions in the small intestine, but other organs may also be affected. Major symptoms may include abdominal pain, diarrhea, and/or weight loss. Intestinal lesions may break through the wall of the bowel (perforation), a potentially life-threatening complication. The exact cause of Degos disease is unknown. Resources Digestive Disease National Coalition 507 Capitol Court Suite 200 Washington, DC 20002

8. Kypros-Net ESearch Degos Patients' Support Network Advice, support, news, and a forum for patients with Degos disease (Malignant Atrophic Papulosis), their families http://tmsyn.wc.ask.com/r?t=an&s=hb&uid=24312681243126812&sid=343126

9. Diagnosing Degos - DegosDisease.com Burrow JN, Blumbergs PC, Iyer PV kohlmeierdegos disease a multisystem Sotrel A, Lacson AG, Huff KR Childhood kohlmeier-degos disease with atypical http://www.degosdisease.com/information/forpros/diagnosing-degos/synonyms_relate

Degos Disease Diagnosing Degos Degos disease (malignant atrophic papulosis) is a rare progressive, small and medium size arterial occluding disease, leading to tissue infarction initially involving the skin and later the gastrointestinal, ocular and central nervous systems. The disease is characterized by papules that develop porcelain-white centres and telangiectatic borders. This is the clue to the underlying disease which can affect the gastrointestinal tract and central nervous system and may lead to death. The skin biopsy places the pathologist at the centre of the diagnostic evaluation. Background In 1941, in an article entitled "Multiple Hautrekrosen bei Thromboangiitis obliterans," Kohlmeier described a case of a disease that has now been termed malignant atrophic papulosis (MAP) or Degos disease (DD). Degos recognized it as a distinct clinical entity in 1942. Broadly speaking, DD is a vasculopathy or an endovasculitis. It is an occlusive arteriopathy involving small-calibre vessels. Specifically, it is a progressive, small- and medium-size arterial occluding disease, leading to tissue infarction and initially involving the skin. DD occurs both in a limited benign, cutaneous form and in a lethal multiorgan, systemic variant. In the skin, DD initially manifests with erythematous, pink or red papules. These papules heal to leave scars with pathognomonic, central, porcelain white atrophic centers. These papules usually have a peripheral telangiectatic rim.

10. Malignant Atrophic Papulosis (Kohlmeier-Degos Disease) In Malignant atrophic papulosis (kohlmeierdegos disease) in childhood FA Horner, GJ Myers, DA Stumpf, BJ Oseroff and BH Choi http://tmsyn.wc.ask.com/r?t=an&s=hb&uid=24312681243126812&sid=343126

11. Degos Disease Synonyms. Degos Syndrome. DegosKohlmeier Disease. kohlmeier-degos disease. Malignant Atrophic Papulosis http://tmsyn.wc.ask.com/r?t=an&s=hb&uid=24312681243126812&sid=343126

12. Degos' Disease Information Diseases Database Degos disease,Erythrokeratoderma en cocardes,kohlmeierdegos disease,Malignantatrophic papulosis, Disease Database Information. http://www.diseasesdatabase.com/ddb29425.htm

Diseases Database Index Sponsors Contact ... Previous Page Degos' disease information Search 4 synonyms or equivalents were found. Degos' disease aka/or Erythrokeratoderma en cocardes aka/or Kohlmeier-Degos disease aka/or Malignant atrophic papulosis may cause or feature (Follow link for list.) belong(s) to the category of (Follow link for list.) No UMLS definitions. Degos' disease: specific web sites Send Degos' disease to medical search engines (JavaScript enabled browsers only.) If your browser has no JavaScript you can still use these: Search using Internet medical databases Search using Internet search engines (non-specialist) We subscribe to the HONcode principles of the Health On the Net Foundation Valid XHTML 1.0 Served 2005-09-09 09:54:25 View metadata Last major update 2005-09-03. The medical information here is presented for education, background reading and general interest. The Diseases Database is not a diagnostic or clinical decision-making tool. Please consult your own licensed physician regarding diagnosis and treatment of any medical condition! Content is not asserted complete or error free, please see also our

13. Degos' Disease Information Diseases Database Degos' disease Erythrokeratoderma en cocardes kohlmeierdegos disease Malignant atrophic papulosis, Disease Database Information http://tmsyn.wc.ask.com/r?t=an&s=hb&uid=24312681243126812&sid=343126

14. Disease, Medication, Symptom Etc Database Index : K Diseases Database Kohler s second disease see Freiberg s disease kohlmeierdegos disease see Degos disease Kohlschutter syndrome Koilonychia http://www.diseasesdatabase.com/disease_index_k.asp

Diseases Database Index Sponsors Contact ... Previous Page Disease, medication, symptom etc database index : K Search Kabuki make-up syndrome Kahler's disease see Myeloma Kala-Azar see Visceral leishmaniasis Kallmann syndrome Kanamycin Kandinsky syndrome Kanner's syndrome see Autism Kanzaki disease see Schindler disease Kaolin Kaposi varicelliform eruption Kaposiform hemangioendothelioma ... Kaposi's sarcoma Karaya gum see Sterculia Karenitecin Kartagener's syndrome Karyotype disorders see Chromosomal abnormalities Kasabach-Merritt syndrome Kaschin-Beck disease Kashin-Beck disease see Kaschin-Beck disease Katayama fever see Schistosoma japonicum Kaufman-McKusick syndrome Kava root extract Kawasaki disease Kayser-Fleischer ring see Fleischer-Kayser ring Kearns-Sayre syndrome Kedani fever see Scrub typhus Keller syndrome see Opitz-Kaveggia syndrome Keloid Keloidal blastomycosis see Lobomycosis Kemerovo tick fever Kemerovo virus see Kemerovo tick fever Kennedy's disease Kenny-Caffey-Linarelli syndrome Kenya tick typhus see Boutonneuse fever Keratinizing cyst see Epidermal inclusion cyst Keratinocyte growth factor see Palifermin Keratinocyte growth factor 2 Keratitis Keratitis-ichthyosis-deafness syndrome, autosomal dominant

15. Degos Disease - Quest Diagnostics Patient Health Library Synonyms. Degos Syndrome. DegosKohlmeier Disease. kohlmeier-degos disease. Malignant Atrophic Papulosis http://tmsyn.wc.ask.com/r?t=an&s=hb&uid=24312681243126812&sid=343126

16. CNS Involvement In Malignant Atrophic Papulosis (Kohlmeier-Degos Disease): Vascu CNS involvement in malignant atrophic papulosis (kohlmeierdegos disease)vasculopathy and coagulopathy. DK Dastur, BS Singhal and HJ Shroff http://jnnp.bmjjournals.com/cgi/content/abstract/44/2/156

HOME HELP FEEDBACK SUBSCRIPTIONS ... TABLE OF CONTENTS Author Keyword(s) Vol Page [Advanced] This Article Submit a response Alert me when this article is cited Alert me when eLetters are posted Alert me if a correction is posted Services Email this link to a friend Similar articles in this journal Similar articles in PubMed Alert me to new issues of the journal ... Cited by other online articles PubMed PubMed Citation Articles by Dastur, D. K. Articles by Shroff, H. J. Journal of Neurology, Neurosurgery, and Psychiatry, 1981, Vol 44, 156-160 PAPERS CNS involvement in malignant atrophic papulosis (Kohlmeier-Degos disease): vasculopathy and coagulopathy DK Dastur, BS Singhal and HJ Shroff The clinical features in a 42 year old man with malignant atrophic papulosis with CNS involvement are described. They included mental dysfunction, paraesthesiae, weakness of left limbs, with pyramidal tract

17. JNNP Online -- Table Of Contents (44 [2]) CNS involvement in malignant atrophic papulosis (kohlmeierdegos disease)vasculopathy and coagulopathy DK Dastur, BS Singhal, and HJ Shroff http://jnnp.bmjjournals.com/content/vol44/issue2/

HOME HELP FEEDBACK SUBSCRIPTIONS ... SEARCH TABLE OF CONTENTS Author Keyword(s) Vol Page [Advanced] Only Abstracts available for this issue Other Issues: February 1981 (Volume 44, Number 2). [Index by author] Papers Letters Find articles in this issue containing these words: [Search ALL Issues] To see an article , click its [Full Text] link. To review many abstracts , check the boxes to the left of the titles you want, and click the 'Get All Checked Abstract(s)' button. To see one abstract at a time , click its [Abstract] link. Papers: Alterations in protein synthetic capability of nerve cells in Alzheimer's disease DM Mann, D Neary, PO Yates, J Lincoln, JS Snowden, and P Stanworth J Neurol Neurosurg Psychiatry 1981; 44: 97-102. [Abstract] Panencephalopathic type of Creutzfeldt-Jakob disease: primary involvement of the cerebral white matter T Mizutani, A Okumura, M Oda, and H Shiraki J Neurol Neurosurg Psychiatry 1981; 44: 103-115.

18. Entrez PubMed A 45 year old female patient presented with the cutaneous manifestations ofmalignant atrophic papul http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=PubMed&list_uids=1

19. Entrez PubMed kohlmeierdegos disease, or malignant atrophic papulosis, is a rare and clinicallydistinctive vascu http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?cmd=Retrieve&db=PubMed&list_uids=2

20. DEGOS DISEASE: Contact A Family - For Families With Disabled Children: Informat Degos disease Malignant Atrophic Papulosis kohlmeierdegos disease. Degos diseaseis a rare inherited condition first described by Kohlmeier in 1941 and http://www.cafamily.org.uk/Direct/d19.html

printer friendly DEGOS DISEASE home how we can help medical information index of conditions ... how you can help Did you find this page helpful? yes no Degos disease: Malignant Atrophic Papulosis: Kohlmeier-Degos disease Degos disease is a rare inherited condition first described by Kohlmeier in 1941 and Degos in 1942. There are thought to have been about 150 cases of the condition reported in medical literature. The most severe form is Systemic Degos disease affecting children and adolescents with most cases occurring in young adults. Benign Degos disease also affects adults. Systemic Degos disease affects a number of body systems: Skin - pink or red papules (solid raised lesions) primarily on the trunk and limbs healing to leave white scars; Gastrointestinal - abdominal pain, nausea, vomiting, diarrhoea or constipation and, in the later stages, intestinal perforation and haemorrhage may occur; Neurological - manifestations involve the peripheral and central nervous systems leading to headaches, dizziness, seizures, hemiplegia (total or partial paralysis of one side of the body), aphasia (loss or impairment of the power to use or comprehend words), paraplegia (paralysis of the lower half of the body), and gaze palsy (partial or complete inability to move the eyes to all directions of gaze); Ocular - ptosis (drooping of the upper eyelid), optic neuritis (inflammation of optic nerves), diplopia (double vision) and visual field defects may occur.

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