Extractions: 15 April 1996 Table of Contents Creutzfeldt-Jakob disease (CJD) is a rare and fatal neuro-degenerative disease. The clinical presentation includes dementia, myoclonus and progressive motor dysfunction. Death usually occurs within a year of the onset of symptoms. CJD is transmitted in humans in rare instances, and the disease can be dormant for as long as 30 years. The average age of onset is 60 years, but there are recorded instances of onset as early as 16 years, and as old as 80 (1-5) . The causative agent has not been identified, but slow viruses of the central nervous system (5) and infective proteinaceous particles or prions (4) have both been postulated as the agent responsible for the disease. There is no current treatment for CJD. Diagnosis is based on clinical signs, characteristic EEG changes, brain biopsy and postmortem histopathologic findings (1,6) . Genetic predisposition to the disease is associated with mutations in the prion protein gene. Concerns have been raised regarding the possible transmissibility of CJD through transfusion of blood or organ transplants. In response to this, the following review of Canadian mortality data has been undertaken to search for clustering of CJD by age, sex or geography.
ACLS -- Sign In Page Keywords creutzfeldtjacob disease, spongiform encephalopathy, prion, creutzfeldt-jacob disease (CJD) is a rare and transmissible neurological disorder http://www.annclinlabsci.org/cgi/content/full/31/2/211
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Creutzfeldt-Jacob Disease Cases The bovine spongiform encephalopathy and the variant creutzfeldtjacob disease cases in the Mediterranean countries. http://www.a-nutritional-supplements.com/conf04a25.htm
Extractions: Athens, 21 - 23 April 2004 Shortly after the identification of Bovine Spongiform Encephalopathy (BSE) in cattle, concerns emerged that this disease could be transmitted to humans consuming meat or meat products. Such concerns have been exacerbated by confirmation that the infectious agent, a prion isolated from BSE-infected cattle, shares a number of characteristic biological and structural features with the infectious agent of variant Creutzfeldt-Jacob disease (vCJD) in humans.
Disease - Creutzfeldt-Jacob Disease - Hartford, Connecticut Disease creutzfeldt-jacob disease - courtesy of Saint Francis Care of Hartford, Connecticut, contemporary medicine with major clinical concentrations in http://www.saintfranciscare.com/11765.cfm
Extractions: Central nervous system Definition: Creutzfeldt-Jacob disease is a disorder involving rapid decrease of mental function and movement. These are abnormalities believed to be caused by damage done to the brain by a protein called a prion. This protein folds abnormally, and seems to encourage other proteins to become similarly misshapen, affecting their ability to function. Alternative Names: Transmissible Spongiform Encephalopathy; New variant CJD - "the human form of mad cow disease" Causes And Risk: Creutzfeldt-Jakob disease can occur sporadically (for no known reason), as a result of exposure to contaminated products. Rarely, it can be genetically inherited. The disorder itself is rare, occurring in about 1 out of 1 million people. It usually first appears in midlife, beginning between ages 20 and 70, with average age at onset of symptoms in the late 50s. However, some cases have occurred in adolescents who have received
Sporadic Creutzfeldt-Jacob Disease - General Practice Notebook sporadic creutzfeldtjacob disease. Sporadic CJD accounts for over 90% of cases of human prion disease. The disease occurs worldwide with an annual http://www.gpnotebook.co.uk/cache/1295319113.htm
Extractions: sporadic Creutzfeldt-Jacob disease Sporadic CJD accounts for over 90% of cases of human prion disease. The disease occurs worldwide with an annual incidence of one case per million population. There are no known environmental risk factors. Most patients with sporadic CJD are homozygous for methionine at the polymorphic position 129 in the prion protein.
The Dictionary Of Cell And Molecular Biology - Online! creutzfeldtjacob disease. Rare fatal presenile dementia of humans, similar to kuru and other slow viruses. Method of transmission unknown. http://www.mblab.gla.ac.uk/~julian/dict2.cgi?1578
GE Creutzfeldt-Jacob Disease Ken Follett. Hyperfiction. Gab Eti Orgrease, Bullamanka, NY, Preservation of Single Occupancy Structures. http://www.geocities.com/SoHo/Cafe/5836/gecjd.html
Extractions: There was a letter in my mailbox last month about a case of spongiform encephalopathy a.k.a. Creutzfeldt-Jacob disease in a guy who ate squirrel brains. I should make clear, Creutzfeldt-Jakob disease is NOT Mad Cow Disease. MCD (bovine spongiform encephalopathy) is one of several prion diseases. A statistical excess of CJD has been seen in people who ate squirrel brains. That is, in a relatively small population there were more cases of CJD than one would expect, and the small population in question ate squirrel brains. Does this mean that squirrels have prion diseases that are contagious to humans? Shit if I know? There was no evidence that the squirrels in question had a prion disease. In fact, there's no evidence that squirrels ever get prion diseases. On the other hand, nobody has looked very closely at squirrel brains. Was this an encyclopedic blip? Who knows? With rare diseases like this, blips happen, and can be real bitches to sort out. CJD occurs in one in a million. There are approximately 250 cases of CJD in the USA per year. It would therefore not be unexpected to see a case of CJD in a human being who consumed an excessive number of squirrel brains. Indeed, it would be remarkable to NOT see any cases of CJD in squirrel brain eaters. More people than you would suspect eat squirrel brains. It is considered a delicacy. Apparently squirrel brains are very common in some parts of the country.
Forum On Nutrition And Exercise: Creutzfeldt-Jacob Disease About creutzfeldtjacob disease I know use of HGH in healthy humans was banned after 4 people contracted creutzfeldt-jacob disease. http://www.thebody.com/Forums/AIDS/Nutrition/Archive/Alternative/Q150003.html
Extractions: Please Note: Due to volume considerations, not all questions can be answered. Questions most likely to be answered will be those of general interest to a broad group of visitors to this forum. Questions pertaining to a specific case; requests for diagnosis, medical advice, or second opinion; or requests for opinions about untested alternative therapies will generally not be answered. Ask the Experts about Nutrition and Exercise Aug 30, 2003 Hi Nelson Great work you are doing here! About Creutzfeldt-Jacob Disease... I know use of HGH in healthy humans was banned after 4 people contracted Creutzfeldt-Jacob Disease. Does the HGH that is now manufactured totally free of the risk of this and other viruses? Response from Mr. Vergel Yes, thank GOD! Nelson Please remember that this forum is designed for educational purposes only, and experts are not engaged through this forum in rendering legal or medical advice or professional services. Experts appearing on this page are independent and are solely responsible for editing and fact-checking their material. Neither The Body nor any sponsor is the publisher or speaker of posted visitors' questions or the experts' material. Questions and messages posted to this forum are not statements of advice, opinion, or information of The Body, Body Health Resources Corporation or any sponsor of this forum. While neither The Body nor Body Health Resources Corporation regularly reviews posted content, we reserve the right to delete, move, or edit postings if we deem it appropriate under the circumstances. Visitors submitting questions remain solely responsible for the content of their messages.
Extractions: Contact: Jane Duffield Patients and medical professionals may call 1-800-533-UPMC (8762) for more information. Telephone: Fax: CREUTZFELDT-JACOB DISEASE INFORMATIONAL RELEASE PITTSBURGH, June 12, 2002 CJD In April 2001 a patient had surgery at UPMC Presbyterian to treat a condition of the nervous system. The surgical instruments were sterilized with standard procedures following the surgery. In the first quarter of 2002, the patient died from progression of a neurological disorder. Following the patient's death it was determined upon autopsy, for the first time, that the patient had Creutzfeldt-Jacob Disease (CJD). This disease is believed to be transmitted by an infectious protein, or prion. Prions may not be eliminated by standard instrument sterilization processes. The instruments used in the patient's surgery presented an extremely low risk of transmitting CJD to patients who had neurosurgery with these instruments during the period from April 17, 2001 to April 6, 2002. There are only a very small number of reported cases of CJD developing after exposure of a patient to instruments used in a prior surgery on an individual with CJD, the most recent being in Europe in 1976. No such cases have been reported in the United States since the adoption of the standard sterilization techniques which were in use at the time of the patient's operation in April of 2001.
Gastroenterology Nursing - UserLogin creutzfeldtjacob disease/Mad Cow Disease A Helpless Vigil The incidence is questionable because creutzfeldt-jacob disease is not a Centers of Disease http://www.gastroenterologynursing.com/pt/re/gastronurse/fulltext.00001610-20050
Creutzfeldt-Jacob Disease Obituary creutzfeldtjacob disease Obituary. In the Sunday May 18 New York Times an obituary was published for Joanie Westie, a Big Star in the World of Roller http://www.organicconsumers.org/cjdobit.html
Extractions: In the Sunday May 18 New York Times an obituary was published for Joanie Westie, a "Big Star in the World of Roller Derbies" who died May 10 at age 62. The interesting part is that, according to her husband, Nick Scopas, she died of a "rare brain disease", you guessed it, Creutzfeldt-Jacob disease. The Times makes no further mention of the cause of death, nor does it remind its readers that this is the same disease that caused such a furor among the French when a few of their citizens died of it. The reason for the French ire was of course that scientists believe that CJ disease is linked to Mad Cow disease (bovine spongiform encephalopathy) The furor resulted in the banning of British beef from import into the EU and the collapse of the British beef industry. This was reported on the front page of the New York Times. Is it that NYT editors don't read their own articles, or are they just being loyal protectors for agri-business interests? And I also wonder if the family is aware of the CJ - Mad Cow connection? If not, may be somebody in California should tell them (or their attorney). They live in Hayward California, near San Francisco. In addition to her husband, Ms. Westie was survived by two step children - Tracy Munoz of Hayward and Nick Scopas Jr. of Manteca CA.
Extractions: News Campaigns GE Food Organics ... email this page February, 2001 Annals of Clinical and Laboratory Science Vol. 31 no. 2 p. 211-2 Creutzfeldt-Jacob Disease (CJD) is a rare and transmissible neurological disorder, which has been increasing in frequency in the United States over the past two decades. [...] We report 7 cases of CJD from North Shore University Hospital, a community-based teaching institution that serves Nassau County on Long Island, NY. These cases were diagnosed and died during the 12-mo period between mid-June 1999 to midJune 2000... These data suggest a CJD death rate in Nassau County... approximately 6 times the national rate. During the previous 1-yr period, no case of CJD was diagnosed in our laboratory [...] The authors are concerned that the number of CJD cases in our catchment area appears to have increased dramatically during the 12-mo period. [...] News Campaigns GE Food Organics ... Site Map Organic Consumers Association
BBC News | HEALTH | VCJD And BSE - The Link vCJD is the human form of mad cow disease. creutzfeldtjacob disease is an untreatable and invariably fatal disease in humans which is similar to BSE in http://news.bbc.co.uk/2/hi/health/967133.stm
Extractions: Creutzfeldt-Jacob disease is an untreatable and invariably fatal disease in humans which is similar to BSE in cattle and scrapie in sheep. The diseases are together called "spongiform encephalopathies", because they all reduce the brain to the same spongy appearance, with gaps appearing within the tissue. The type of CJD associated with BSE in cattle is termed "variant CJD", and is distinctively different from standard CJD - which emerges in between 25 and 60 UK adults each year, normally in people aged over 55. Variant CJD began to emerge and be diagnosed in the mid-1990s - there have been 73 confirmed cases so far, with just under a dozen probable cases which have yet to be confirmed, either because the patient is still alive, or because the post mortem has yet to take place.
Healthinmind/Menthal Health Disorders/Dementias/Creutzfeld-Jacob creutzfeldtjacob disease. This type of dementia, like Alzheimer s or Huntington s, is caused by organic changes in the brain, but in this case the changes http://healthinmind.com/english/creutz-ja.htm
NewsFromRussia.Com Japan: First Human Victim Of Mad Cow Disease The human variant of creutzfeldtjacob disease has only been confirmed or deemed probable in 167 other people worldwide, virtually all of them in Britain http://newsfromrussia.com/science/2005/02/04/58098.html
Extractions: Pravda.ru Russia Science and Health World ... Opinion pravda.ru sites ... News from Russia /English/ PhotoReports /English/ Forum /English/ FunReports /English/ Pravda.Ru /Portuguese/ Pravda.Ru /Russian/ News /Russian/ Forum /Russian/ Politics /Russian/ World /Russian/ Culture /Russain/ Science /Russian/ Economics /Russian/ Society /Russian/ Districts /Russian/ Accidents /Russian/ Sport /Russian/ Market /Russian/ Lady Pravda.Ru /Russian/ Fark.Ru /Russian/ Health /Russian/ Russia World Science and Culture Accidents ... About Pravda.RU:Science and Culture:More in detail A Japanese man who died in December is believed to be the first person in Japan to die of the human variant of mad cow disease , Japanese Health Ministry officials said.
